LIST OF CONTRIBUTORS . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . IX
ABOUT THE EDITORS . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . XIII
Introduction: ARRHYTHMOGENIC RIGHT VENTRICULAR CARDIOMYOPATHY/
DYSPLASIA CLARIFIED . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 1
Gaetano Thiene, Andrea Nava, Frank I. Marcus
CHAPTER 1 ADVANCES IN GENETICS: DOMINANT FORMS . . . . . . . . . . . . . . . . . . . . . 7
Alessandra Rampazzo, Gian Antonio Danieli
CHAPTER 2 ADVANCES IN GENETICS: RECESSIVE FORMS . . . . . . . . . . . . . . . . . . . . . 15
Nikos Protonotarios, Adalena Tsatsopoulou
CHAPTER 3 GENOTYPE-PHENOTYPE CORRELATIONS . . . . . . . . . . . . . . . . . . . . . . . . . . 21
Barbara Bauce, Andrea Nava
CHAPTER 4 AUTOPSY AND ENDOMYOCARDIAL BIOPSY FINDINGS . . . . . . . . . . . 29
Cristina Basso, Gaetano Thiene
CHAPTER 5 CELL ADHESION PATHOLOGY . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 45
Jeffrey E. Saffitz
CHAPTER 6 ULTRASTRUCTURAL SUBSTRATES . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 53
Elzbieta Czarnowska, Mila Della Barbera, Gaetano Thiene, Marialuisa Valente, Cristina Basso
CHAPTER 7 TRANSGENIC ANIMAL MODELS . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 61
Matteo Vatta, Zhao Yang, Jeffrey A.Towbin
CHAPTER 8 SPONTANEOUS ANIMAL MODELS . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 69
Philip R. Fox, Cristina Basso, Gaetano Thiene, Barry J. Maron
CHAPTER 9 POSSIBLE CAUSATIVE OR CONTRIBUTING ROLE OF VIRUSES . . . 79
Fiorella Calabrese, Elisa Carturan, Gaetano Thiene, Jeffrey A.Towbin
CHAPTER 10 DIAGNOSIS: TASK FORCE CRITERIA INCLUDING MODIFICATIONS
FOR FAMILY MEMBERS . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 87
Deirdre Ward, Petros Syrris, Srijita Sen-Chowdhry,William J. McKenna
Indice VII
CHAPTER 11 STRENGTHS AND WEAKNESSES OF THE TASK FORCE CRITERIA –
PROPOSED MODIFICATIONS . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 97
Frank I. Marcus, Duane Sherrill
CHAPTER 12 IDIOPATHIC RIGHT VENTRICULAR OUTFLOW TRACT
TACHYCARDIA . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 105
Gianfranco Buja, Barbara Ignatiuk,Thomas Wichter, Domenico Corrado
CHAPTER 13 ELECTROCARDIOGRAPHIC MANIFESTATIONS . . . . . . . . . . . . . . . . . . . . 121
Wojciech Zareba, Katarzyna Piotrowicz, Pietro Turrini
CHAPTER 14 ECHOCARDIOGRAPHY . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 129
Danita Yoerger-Sanborn, Michael H. Picard, Barbara Bauce
CHAPTER 15 MR AND CT IMAGING . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 135
Harikrishna Tandri, Hugh Calkins, David A. Bluemke
CHAPTER 16 DIAGNOSTIC ROLE OF ANGIOGRAPHY . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 147
Thomas Wichter, Julia Indik, Luciano Daliento
CHAPTER 17 ELECTROPHYSIOLOGIC STUDY INCLUDING ELECTROANATOMIC
MAPPING . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 159
Domenico Corrado, James Daubert, Cristina Basso, Gianfranco Buja, Gaetano Thiene
CHAPTER 18 RISK STRATIFICATION AND ANTIARRHYTHMIC DRUG THERAPY 171
Thomas Wichter, Domenico Corrado, Matthias Paul
CHAPTER 19 CATHETER ABLATION OF VENTRICULAR TACHYCARDIA . . . . . . . . . 181
Guy Fontaine, Jérôme Lacotte, Françoise Hidden-Lucet, Robert Frank
CHAPTER 20 THE ROLE OF THE IMPLANTABLE CARDIAC DEFIBRILLATOR
IN THE MANAGEMENT . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 189
Olaf Hedrich, Gianfranco Buja, Domenico Corrado, Mark S. Link,Thomas Wichter,
N.A. Mark Estes III
CHAPTER 21 MANAGEMENT OF HEART FAILURE . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 199
Elzbieta Katarzyna Wlodarska, Marek Konka
CHAPTER 22 SUDDEN DEATH IN YOUNG ATHLETES . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 205
Domenico Corrado, Cristina Basso, Gaetano Thiene
SUBJECT INDEX . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 213