LIST OF CONTRIBUTORS . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . IX
ABOUT THE EDITORS . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . XIII
Introduction: ARRHYTHMOGENIC RIGHT VENTRICULAR CARDIOMYOPATHY/
DYSPLASIA CLARIFIED . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 1
Gaetano Thiene, Andrea Nava, Frank I. Marcus

CHAPTER 1 ADVANCES IN GENETICS: DOMINANT FORMS . . . . . . . . . . . . . . . . . . . . . 7

Alessandra Rampazzo, Gian Antonio Danieli

CHAPTER 2 ADVANCES IN GENETICS: RECESSIVE FORMS . . . . . . . . . . . . . . . . . . . . . 15

Nikos Protonotarios, Adalena Tsatsopoulou

CHAPTER 3 GENOTYPE-PHENOTYPE CORRELATIONS . . . . . . . . . . . . . . . . . . . . . . . . . . 21

Barbara Bauce, Andrea Nava

CHAPTER 4 AUTOPSY AND ENDOMYOCARDIAL BIOPSY FINDINGS . . . . . . . . . . . 29

Cristina Basso, Gaetano Thiene

CHAPTER 5 CELL ADHESION PATHOLOGY . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 45

Jeffrey E. Saffitz

CHAPTER 6 ULTRASTRUCTURAL SUBSTRATES . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 53
Elzbieta Czarnowska, Mila Della Barbera, Gaetano Thiene, Marialuisa Valente, Cristina Basso
CHAPTER 7 TRANSGENIC ANIMAL MODELS . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 61

Matteo Vatta, Zhao Yang, Jeffrey A.Towbin

CHAPTER 8 SPONTANEOUS ANIMAL MODELS . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 69

Philip R. Fox, Cristina Basso, Gaetano Thiene, Barry J. Maron

CHAPTER 9 POSSIBLE CAUSATIVE OR CONTRIBUTING ROLE OF VIRUSES . . . 79

Fiorella Calabrese, Elisa Carturan, Gaetano Thiene, Jeffrey A.Towbin

CHAPTER 10 DIAGNOSIS: TASK FORCE CRITERIA INCLUDING MODIFICATIONS
FOR FAMILY MEMBERS . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 87
Deirdre Ward, Petros Syrris, Srijita Sen-Chowdhry,William J. McKenna

Indice VII

CHAPTER 11 STRENGTHS AND WEAKNESSES OF THE TASK FORCE CRITERIA –
PROPOSED MODIFICATIONS . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 97
Frank I. Marcus, Duane Sherrill

CHAPTER 12 IDIOPATHIC RIGHT VENTRICULAR OUTFLOW TRACT

TACHYCARDIA . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 105
Gianfranco Buja, Barbara Ignatiuk,Thomas Wichter, Domenico Corrado

CHAPTER 13 ELECTROCARDIOGRAPHIC MANIFESTATIONS . . . . . . . . . . . . . . . . . . . . 121

Wojciech Zareba, Katarzyna Piotrowicz, Pietro Turrini

CHAPTER 14 ECHOCARDIOGRAPHY . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 129

Danita Yoerger-Sanborn, Michael H. Picard, Barbara Bauce

CHAPTER 15 MR AND CT IMAGING . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 135

Harikrishna Tandri, Hugh Calkins, David A. Bluemke

CHAPTER 16 DIAGNOSTIC ROLE OF ANGIOGRAPHY . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 147

Thomas Wichter, Julia Indik, Luciano Daliento

CHAPTER 17 ELECTROPHYSIOLOGIC STUDY INCLUDING ELECTROANATOMIC
MAPPING . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 159
Domenico Corrado, James Daubert, Cristina Basso, Gianfranco Buja, Gaetano Thiene
CHAPTER 18 RISK STRATIFICATION AND ANTIARRHYTHMIC DRUG THERAPY 171

Thomas Wichter, Domenico Corrado, Matthias Paul

CHAPTER 19 CATHETER ABLATION OF VENTRICULAR TACHYCARDIA . . . . . . . . . 181

Guy Fontaine, Jérôme Lacotte, Françoise Hidden-Lucet, Robert Frank

CHAPTER 20 THE ROLE OF THE IMPLANTABLE CARDIAC DEFIBRILLATOR
IN THE MANAGEMENT . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 189
Olaf Hedrich, Gianfranco Buja, Domenico Corrado, Mark S. Link,Thomas Wichter,
N.A. Mark Estes III

CHAPTER 21 MANAGEMENT OF HEART FAILURE . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 199

Elzbieta Katarzyna Wlodarska, Marek Konka

CHAPTER 22 SUDDEN DEATH IN YOUNG ATHLETES . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 205

Domenico Corrado, Cristina Basso, Gaetano Thiene

SUBJECT INDEX . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . 213

 

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